Table 1.

Baseline Clinical Characteristics of Individual Patients

Patient‐Family	1‐a	2‐b	3‐c	4‐c	5‐d	6‐e	7‐f	8‐g	9‐h	10‐h	11‐i	12‐d
Age‐sex	34‐M	49‐M	29‐F	18‐M	43‐F	39‐M	38‐F	46‐F	29‐M	65‐M	54‐M	44‐F
Muscular impairmenta	2	3	1	1	1	2	3	2	2	1	1	1
Heart failureb	No	No	No	No	No	No	No	No	No	No	No	No
Syncope	No	No	No	No	No	No	No	No	No	No	No	No
Aborted SCD	No	No	No	No	No	No	No	No	No	No	No	No
SCD‐BrS family history	No	No	No	No	No	No	No	No	No	No	No	No
Pacemaker	No	Yes	No	No	No	No	No	No	No	No	No	No
ICD	No	No	No	No	No	No	No	No	No	No	No	No

^aA score of 1 indicates no clinical muscular impairment, 2 minimal signs without distal weakness except for digit flexor, 3 distal weakness without proximal weakness except for elbow extensors, 4 moderate proximal weakness, and 5 severe proximal weakness;

^bNew York Heart Association (NYHA) functional class II to IV.

M = male; F = female; SCD = sudden cardiac death; ICD = implantable cardioverter‐defibrillator.