Table 2.
Feature | Value |
---|---|
Age at diagnosis (years)a | 18.1 (8.7) |
Sex | |
Female | 3/7 (43%) |
Male | 4/7 (57%) |
Hepatosplenomegaly | 6/6 (100%) |
Growth deficit | 5/7 (71%) |
Arthritis | 6/6 (100%) |
Anemia | 5/6 (83%) |
Hemoglobin (g/L)a | 8.2 (2.1) |
Serum zinc (μm/L)a | 153.4 (35.4) |
Calprotectin (g/L)b | 4.9 (1.5–6.1) |
Mean (standard deviation).
Median (1st quartile − 3rd quartile).