Figure 2.

(A) Computed tomography (CT) through the lung apices demonstrating classical features of pleuroparenchymal fibroelastosis (PPFE), including pleural thickening, subpleural consolidation with coarse reticulation, and striking traction bronchiolectasis/bronchiectasis. (B) Coronal reconstruction of the same study as in A showing bilateral upper zone PPFE that extends caudally to the level of the fourth rib in the right hemithorax (arrowhead). Marked volume loss can be judged by elevation of the interlobar fissures (arrows). (C) Unequivocal progression of PPFE evident on a follow-up CT scan 2 years later. (D) Coronal CT image of bilateral apical pleural caps, more prominent on the right (arrow).