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. Author manuscript; available in PMC: 2021 Jan 6.
Published in final edited form as: Alzheimers Dement. 2020 Jan 6;16(1):22–36. doi: 10.1016/j.jalz.2019.06.4947

Table 3.

Clinical Phenotypes and Confidence Rating

Clinical Phenotypes (primary, and secondary and tertiary if applicable)
Normal neurologic functioning
Behavioral variant frontotemporal dementia
Primary progressive aphasia – agrammatic/nonfluent variant subtype
Primary progressive aphasia – semantic variant subtype
Primary progressive aphasia – logopenic variant subtype
Corticobasal syndrome - typical or variant
Progressive supranuclear palsy/Richardson’s syndrome
Amyotrophic lateral sclerosis
FTD/ALS
MCI - cognitive variants: aMCIsd, aMDmd, naMCIsd, naMCImd
MCI - behavior
MCI - language
MCI - unknown
Alzheimer’s disease dementia Confidence in Primary Clinical Phenotype Diagnosis
Dementia with Lewy bodies 100% (extremely confident)
Parkinson’s disease 90%
Parkinson’s disease with dementia 80%
Multiple system atrophy 70%
Posterior cortical atrophy 60%
Primary psychiatric disorder - Mood 50%
Primary psychiatric disorder - Thought 40%
Primary psychiatric disorder - Personality 30%
Other, specify 20%
10%
0% (not confident at all)