Table 1.
Patient characteristics at baseline
| Characteristics | n/(%) | Mean | SD |
|---|---|---|---|
| Age at first diagnosis (years) | 211 | 62,96 | 13,3 |
| Gender (n) | |||
| Males | 112 (53,1) | ||
| Females | 99 (46,9) | ||
| Smoking status | 210 | ||
| Non-smokers | 106 (50,2) | ||
| Active smokers | 9 (4,3) | ||
| Former smokers | 95 (45,2) | ||
| Pack-years | 206 | 11,01 | 16,2 |
| Family history for lung diseases | |||
| Family history for ILD | 8 (3,8) | ||
| Pulmonary function | |||
| FVC (% predicted) | 209 | 72,68 | 21,20 |
| FVC (L) | 207 | 2,41 | 0,92 |
| FEV1 (% predicted) | 210 | 76,82 | 20,12 |
| FEV1/FVC% | 209 | 81,94 | 8,52 |
| TLC (L) | 205 | 4,31 | 1,19 |
| TLC (% predicted) | 207 | 74,14 | 15,92 |
| DLCO-SB (% predicted) | 185 | 44,10 | 13,92 |
| 6MWD (m)* | 164 | 373,43 | 112,14 |
| Modified GAP stage [13] | |||
| I | 89,1 | ||
| II | 8,5 | ||
| III | 2,4 | ||
*6 MWT = 6 minutes walking test