Table 1.
Absolute Cell Counts | 80 Cells/mL |
---|---|
Lymphocyte subpopulations (age corrected normal % range) |
% |
CD3+ T cells (52–83) | 1.9 |
CD4+ T cells (31–58) | 1 |
CD8+T cells (16–40) | 0.9 |
CD19+ B cells (5–18) | 0 |
CD16+56+NK cells (5–27) | 94 |
Immunophenotype | T-B-NK+ |
Gene defect | RAG1 |
Serum Immunoglobulins (age corrected normal range) |
g/L |
IgG (270–1100) | <35 |
IgM (20–170) | <5.25 |
IgA (110–115) | <7.83 |
T cell proliferation | PHA- |