Table 2.

Summary of tumor treatment and clinical outcome.

Case	Tumor Stage (Evans)	PRETEXT Stage	Preoperative Chemotherapy	Response RECIST	Resection	Site of Metastasis	Radiotherapy	Postoperative/Retrieval Chemotherapy	Outcome
1	I	PRETEXT 2	none	No	R0		Yes Records not available	vincristine, doxorubicin, cyclophosphamide, cisplatin, ifosfamide, etoposide, irinotecan, temozolomide	DOD
2	IV	PRETEXT 3	cisplatin, doxorubicin	No	None	Lung, Brain	No	irinotecan, vincristine	DOD
3	IV	PRETEXT 3M	vincristine, cisplatin, doxorubicin	Yes CR-lung PR- liver	R0	Lung	Yes 1050cGy to whole lung 1050cGy to abdomen	carboplatin, cyclophosphamide, etoposide	Alive at 8 years after diagnosis
4	IV	PRETEXT 2	vincristine, irinotecan, cisplatin, doxorubicin, 5FU	Yes PR- liver PR-lung	R0	Lung	Yes 1050cGy to whole lung 1200cGy to abdomen 14.5Gy to cavity intra-op after recurrence	ifosfamide, carboplatin, vincristine, cyclophosphamide, doxorubicin HD chemotherapy with autologous SCT Second surgical resection	DOD
5	III	PRETEXT 2	cisplatin, doxorubicin	No	None	Lung	No	pazopanib	DOD
6	III	PRETEXT 3	vincristine, doxorubicin, cyclophosphamide	Yes PR-liver	R1 margin		Yes Proton beam 3000cGy to abdomen	HD chemotherapy with autologous SCT	Alive at 1.5 years after diagnosis

DOD: died of disease. Patient 1 had tumor rupture prior to surgery at diagnosis. In Patients 2 and 5, no resection was performed; however, patients received additional chemotherapy (listed under postoperative/retrieval chemotherapy). CR = complete response; PR = partial response.