Table 1.
Patient characteristics of the study cohort.
| Sex | CFTR Genotype | Age (yr) | BAL cell no. (x106/ml) | NE levels | IL-8 (pg/ml) | Streptococcus spp. | Haemophilus spp. | Escherichia spp. | Staphylococcus spp. | Moraxella spp. | Antibiotic Treatment |
|---|---|---|---|---|---|---|---|---|---|---|---|
| F | p.Phe508del/ p.Phe508del | 1 | 1.2 | 32.46 | 185.45 | − | − | − | − | − | No |
| F | p.Phe508del/ p.Phe508del | 6 | 74.7 | 0.00 | 192.10 | + | − | − | + | − | No |
| F | G551D/G551D | 3 | 1.1 | 54.52 | 276.27 | − | + | − | − | − | No |
| F | G551D/G551D | 4 | 4.2 | 0.00 | 1673.19 | − | − | − | − | − | No |
| F | p.Phe508del/ p.Phe508del | 1 | 3.1 | 0.00 | 1716.03 | - | − | − | − | − | Yes |
| F | p.Phe508del/ p.Phe508del | 2 | 41 | 0.00 | 1745.38 | − | − | − | − | − | No |
| M | p.Phe508del/ p.Phe508del | 3 | 2.7 | 13454.38 | 336.85 | + | − | − | − | Yes | |
| M | p.Phe508del/ p.Phe508del | 4 | 86 | 0.00 | 841.81 | − | − | − | − | − | No |
| M | p.Phe508del/c.2988+1 G > A | 2 | 0.27 | 0.00 | 841.81 | − | + | + | Yes | ||
| M | C489+2 G > T/c.1558 G > T | 1 | 7.5 | 0.00 | 109.08 | + | − | − | Yes | ||
| M | p.Phe508del/ p.Phe508del | 3 | 15 | 0.00 | 512.74 | + | − | − | − | + | Yes |
| M | p.Phe508del/ p.Phe508del | 3 | 55.1 | 227.71 | 1162.45 | + | − | − | Yes |