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The 1-deoxygalactonojirimycin (DGJ)-derived PCs for GLB1 deficiency. (A) Methyl 6-{[N2-(dansyl)-N6-(1,5-dideoxy-d-galactitol-1,5-diyl)-L-lysyl]amino} hexanoate (DLHex-DGJ); (B) N-(dansylamino) hexylaminocarbonylpentyl-1,5-dideoxy-1,5-imino-d-galactitol; (C) N-nonyl-deoxygalactonojirimycin (NN-DGJ); and (D) 5N,6S-(N-butyliminomethylidene)-6-thio-1-deoxygalactonojirimycin (6S-NBI-DGJ).
