Table 4.
Clinical immunology results.
| Patient ID | IgG# (g/L) | IgM (g/L) | IgA (g/L) | Lymfocyte count (cells/μL WB) | B cells (CD19+; cells/μL) | NK cells (CD56+; cells/μL) | T cells (CD3+; cells/μL) | CD4 (cells/μL) | CD8 (cells/μL) | CD4/CD8-ratio | Isohaemagglutinin IgM/IgG |
|---|---|---|---|---|---|---|---|---|---|---|---|
| P1 | 2.9 | <0.2 | BD | 881 | 63 | 29 | 774 | 290 | 435 | 0.67 | NP |
| P2 | 2.9 | 0.32 | BD | 5,800 | 160 | 40 | 1,200 | 800 | 350 | 2.4 | NP |
| P3 | 1.1 | <0.2 | BD | 908 | 68 | 109 | 717 | 430 | 230 | 1.88 | NP |
| P4 | 0.3 | <0.2 | BD | 2,140 | 738 | 257 | 1,119 | 693 | 393 | 1.76 | NP |
| P5 | 0.9 | <0.2 | BD | 400 | 2 | 46 | 347 | 155 | 153 | 1.01 | After IVIG/after IVIG |
| P6 | * | <0.2 | BD | 493 | 59 | 79 | 281 | 143 | 109 | 1.32 | After IVIG/after IVIG |
| P7 | * | <0.2 | BD | 632 | 15 | 58 | 504 | 215 | 274 | 0.79 | NP |
| P8 | 4.4 | 0.59 | 0.7 | 1,072 | 77 | 93 | 889 | 530 | 264 | 2.01 | Normal |
| P9 | * | <0.2 | BD | 324 | 22 | 25 | 270 | 186 | 74 | 2.51 | NP |
| P10 | 4.2 | * | BD | 266 | 68 | 34 | 156 | 102 | 48 | 2.13 | NP (only after IVIG) |
| P11 | * | <0.2 | BD | 1,147 | 92 | 203 | 848 | 240 | 522 | 0.46 | NP |
| P12 | 3.3 | 0.3 | BD | 516 | 118 | 94 | 285 | 168 | 100 | 1.67 | NP |
| P13 | 0.47 | <0.2 | BD | 1,323 | 106 | 118 | 1,050 | 431 | 562 | 0.77 | Absent A; decreased (B) (both IgM+IgG) |
| P14 | * | <0.2 | BD | 1,600 | 224 | 51 | 1,312 | 853 | 354 | 2.41 | NP |
| P15 | 5.9 | 0.82 | 0.54 | 2,917 | 268 | 76 | 2,482 | 1,633 | 730 | 2.24 | Decreased/decreased |
| P16 | 4.8 | 0.42 | 1.58 | 3,213 | 321 | 112 | 2,757 | 1,566 | 1,023 | 1.53 | Decreased/decreased |
| P17 | 0.7 | 0.15 | BD | 1,877 | 135 | 139 | 1,541 | 925 | 564 | 1.64 | Decreased/decreased |
| P18 | 2.2 | 1.12 | 0.13 | 5,113 | 1,089 | 547 | 3,288 | 1,772 | 1,065 | 1.66 | Decreased/normal |
| P19 | 4.3 | 0.49 | 0.24 | 1,600 | 149 | 210 | 1,182 | 876 | 234 | 3.74 | Decreased/decreased |
| P20 | 7.5 | 0.23 | 3.45 | 249 | 18 | 106 | 123 | 97 | 20 | 4.81 | NP |
No measurement available;
IgG before initiation of immunoglobulin substitution therapy; BD, below detection limit. Reference values: IgGtot (6.9–15.7 g/L); IgM (g/L) (0.55–3.9); IgA (g/L) (BD; below detection limit) (0.8–3.9); Lymfocyte count (cell/μL WB) (1,000–2,800); B cells (CD19+; cells/μL) (70–272); NK cells (CD56+; cells/μL) (52–639); T cells (CD3+; cells/μL) (581–1,895); CD4 (cells/μL) (309–1,140); CD8 (cells/μL) (137–823); CD4/CD8-ratio (PMID: 14962239); NP, not performed; BD; below detection limit.