COL6 loss results in aberrant respiratory function. A: Pressure-volume curves for wild-type (WT) and Col6a1−/− mice. B–F: Quasi-static compliance (B), respiratory system compliance (C), respiratory system resistance (D), tissue damping (E), and tissue elastance (F) measures for WT and Col6a1−/− mice. n = 5 (A–F). *P < 0.05, **P < 0.01, and ***P < 0.001 versus WT.