TABLE 1.

Clinical and Genetic Characteristics

Group	CBD	PSP
Demographics
n	45	108
Male:female ratio	17:18	67:41
Age of onset (year)*	62 ± 9.4	68 ± 7.3
Disease duration (year)	6 ± 2.4	7 ± 3.9
Age at death (year)	67 ± 9.7	76 ± 7.4
Clinical syndrome
CBS	35% (16)	10% (11)
FTD†	42% (19)	22% (23)
Parkinsonism‡	—	10% (11)
RS	22% (10)	58% (63)
Genetics
APOEε2§	18% (8)	19% (21)
APOEε4§	13% (6)	19% (21)
MAPT h1h1	80% (36)	92% (99)
MAPT h1c
0 alleles	29% (13)	27% (29)
1 alleles	53% (24)	42% (45)
2 alleles	18% (8)	31% (34)

^*Mean ± SD.

^†FTD includes bvFTD, FTLD-PPA (PNFA), FTLD-PPA (Logopenic) or FTLD-NOS, AD, Dementia with Lewy bodies, or dementia NOS.

^‡Parkinsonism includes PD, PD with dementia, MSA, Parkinsonism NOS, Motor neuron disease, and clinically suspected ALS.

^§One or more copies.