3’UTR	3’ Untranslated region
A1AT	Alpha-1 antitrypsin
A1ATD	Alpha-1 antitrypsin deficiency
ABC	Adenosine triphosphate binding cassette
AMP	Antimicrobial peptide
ANO1	Anoctamin 1
AP-1	Activator protein 1
ATF6	Activating transcription factor 6
ATP	Adenosine triphosphate
BALF	Bronchoalveolar lavage fluid
CatG	Cathepsin G
CAV1	Caveolin 1
CF	Cystic fibrosis
CFTR	Cystic fibrosis transmembrane conductance regulator
CXCR1	C-X-C Motif Chemokine Receptor 1
ECM	Extracellular matrix
ELANE	Elastase, neutrophil expressed
ELF	Epithelial lining fluid
ER	Endoplasmic reticulum
hMNEI	Human monocyte/neutrophil elastase inhibitor
IPF	Idiopathic pulmonary fibrosis
IRF-1	Interferon regulatory factor 1
MCP-1	Monocyte chemoattractant protein 1
miRNA	Micro RNA
MMP-9	Matrix metalloproteinase 9
MPO	Myeloperoxidase
MRE	Micro RNA responsive element
mRNA	Messenger RNA
NE	Neutrophil elastase
NET	Neutrophil extracellular trap
NF-κB	Nuclear factor kappa-light-chain-enhancer of activated B cells;
ODSH	2-O, 3-O-desulfated heparin
PAMP	Pathogen associated molecular pattern
PR3	Proteinase 3
PRR	Pattern recognition receptor
rAAV	Recombinant adeno-associated viral vector
RNAi	RNA interference
RPTOR	Regulatory-associated protein of mTOR, complex 1
SHIP	Src homology-2 domain-containing inositol 5-phosphatase 1
SLPI	Secretory leukocyte protease inhibitor
TSB	Target site blocker
TGFβ	Transforming growth factor beta
TIMP-1	Tissue inhibitor of metalloproteinase 1
TLR	Toll-like receptor
TOM1	Target of Myb1
TSB	Target site blockers
UPR	Unfolded protein response