(A) Schematic representation of residue substitutions in the NLRP3 protein and reported point mutations. Mutations reported to be involved in Muckle-Wells syndrome and familial cold autoinflammatory syndrome (FCAS) are highlighted in red and blue, respectively.
(B) The domain organization of human PYRIN, indicating the four major domains and residue substitutions. Mutations reported to be involved in familial Mediterranean fever (FMF) are highlighted in red.