Table 3.
Factors involved in the assembly of ETC Complexes I–V
| Complex I | Complex II | Complex III | Complex IV | Complex V | ||||||
|---|---|---|---|---|---|---|---|---|---|---|
| Hsa | Ago | Hsa | Ago | Hsa | Agob | Hsa | Agob | Hsa | Ago | Sce |
| NUBPL | NUBPL | SDHAF1 | SdhAF1 | MZM1L | LYRM7 | CMC1 | Cmc1 | ATPAF1 | Atp11 | |
| NDUFAF2 | NDUFAF2 | SDHAF2 | SdhAF2 | BCS1L | n.d. | CMC2 | Cmc2 | ATPAF2 | Atp12 | |
| NDUFAF3 | NDUFAF3 | SDHAF3 | SdhAF3 | UQCC1 | Cbp3 | COA1 | n.d. | ATP23 | Atp23 | |
| NDUFAF4 | n.d. | SDHAF4 | SdhAF4 | UQCC2 | n.d. | (COA2c) | n.d. | TMEM70 | n.d. | |
| NDUFAF5 | NDUFAF5 | UQCC3 | n.d. | COA3 | n.d. | |||||
| NDUFAF6 | NDUFAF6 | TTC19 | n.d. | COA4 | Coa4 | Atp10 | Atp10 | |||
| NDUFAF7 | NDUFAF7 | COA5 | Coa5 | Nca2 | Nca2 | |||||
| NDUFAF8 | n.d. | – | CcmA | COA6 | Coa6 | |||||
| NDUFAF1a | NDUFAF1 | – | CcmB | COA7 | n.d. | |||||
| TIMMDC1 | n.d. | – | CcmC | COX10 | Cox10 | |||||
| ECSIT | n.d. | – | CcmD | COX11 | Cox11 | |||||
| ACAD9 | n.d. | – | CcmE | COX14 | n.d. | |||||
| TMEM126B | n.d. | – | CcmF | COX15 | Cox15 | |||||
| TMEM186 | n.d. | – | CcmG | COX16 | Cox16 | |||||
| FOXRED1 | n.d. | – | CcmH | COX17 | Cox17 | |||||
| ATP5SL | n.d. | – | CcmI | COX18 | Cox18 | |||||
| DMAC1 | DMAC1 | COX19 | Cox19 | |||||||
| COA1 | n.d. | COX20 | Cox20 | |||||||
| TMEM70 | n.d. | COX23 | Cox23 | |||||||
| AIF | AIFe | PET100 | Pet100Fd | |||||||
| PET117 | Pet117 | |||||||||
| TACO1 | Taco1 | |||||||||
| FASTKD2 | n.d. | |||||||||
| SCO1 / 2 | Sco | |||||||||
| SURF1 | Surf1/Shy1 | |||||||||
See HGNC (mitochondrial respiratory chain complex assembly factors) [59], Guerrero-Castillo et al. [56], and Signes and Fernandez-Vizarra [58]. n.d., not detected
aGenes set in italics are members of the Mitochondrial Complex I Assembly (MCIA) complex (see [60])
bGenes set in bold are encoded in the A. godoyi mitochondrial genome
cExclusively fungal; no human ortholog
dFungal version
eListed under (I) ROS METABOLISM, REGULATION in Additional file 1: Table S1