Imaging findings of the ears with labyrinthine aplasia

Patient	CT/MRI	CLA	Otic Capsule	Middle Ear	Ossicle Anomaly	IAC	Cochlear Nerve	Facial Nerve Course	Jugular Anomaly	Posterior Fossa Anomaly	Skull Base−Other Bone Anomaly
1	+/+	R	Apl	Hypopl	+	Apl	Apl	Aberr	+	Large CPA	Narrow clivus
		L	Apl	Hypopl	+	Apl	Apl	Aberr	+
2	+/−	L	Hypopl	Hypopl	+	Narrow	?	Aberr	+	R CPA arachnoid cyst	Low tegmen tympani, narrow clivus
3	+/+	R	Apl	Hypopl	+	Narrow	Apl	Aberr	+	–	Tegmental defect (L), low tegmen tympani (R), narrow clivus
		L	Hypopl	Hypopl	–	Narrow	Apl	Aberr	–
4	+/+	L	Hypopl	Hypopl	+	Narrow	Apl	Aberr	+	Split brain stem	Narrow clivus
5	+/+	R	Hypopl	Hypopl	?	Narrow	Apl	Aberr	+	Wide 4th v lateral recess	Tegmental defect, narrow clivus
6	+/+	R	Apl	Hypopl	?	Narrow	Apl	Aberr	+	Pontine malformation	Encephalocele
		L	Apl	Hypopl	+	Apl	Apl	Aberr	+
7	+/−	R	Hypopl	N	?	Apl	?	?	+	–	–
		L	Hypopl	N	?	Narrow	?	Aberr	–
8	+/+	R	Hypopl	Hypopl	+	Narrow	Apl	Aberr	–	–	–
9	+/+	R	Hypopl	Hypopl	–	Narrow	Apl	Aberr	–	Chiari 1	–
		L	Hypopl	Hypopl	+	Narrow	Apl	Aberr	+

Note:—MRI indicates MR imaging; R, right; L, left; Apl, aplasia; Hypopl, hypoplasia; N, normal; ?, could not be evaluated in detail; Aberr, aberrant; CPA, cerebellopontine angle; 4th v, fourth ventricle; +/+, both present; +/−, MRI absent; –, not found; CLA, complete labyrinthine aplasia; IAC, internal auditory canal; +, present.