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. Author manuscript; available in PMC: 2021 Mar 1.
Published in final edited form as: Pediatr Pulmonol. 2020 Jan 3;55(3):674–681. doi: 10.1002/ppul.24621

Table 2.

Age and ERT Dose for patients included in Figure 2.

Patient Age at
PFT 1
(years)
ERT dose at PFT 1 Age at
PFT 2
ERT dose PFT 2
1 7.1 20 mg/kg qoweek 17.4 40 mg/kg/week
2 9.0 20 mg/kg/qoweek 16.3 30 mg/kg/week
3 7.8 30 mg/kg/qoweek 10.1 40 mg/kg/week
4 9.0 30 mg/kg/week 12.8 40 mg/kg/week
5 8.1 30 mg/kg/qoweek 11.5 40 mg/kg/week
6 8.2 40 mg/kg/qoweek 12.9 40 mg/kg/week
7 7.8 40 mg/kg/week
8 8.7 40 mg/kg/week
9 7.8 30 mg/kg/qoweek 12.3 40 mg/kg/week
10 8.9 40 mg/kg/week 11.2 40 mg/kg/week
11 6 40 mg/kg/week
12 5.9 40 mg/kg/week
13 5.9 40 mg/kg/week