Table 2.
Clinical manifestations of 34 SIgAD patients.
| Symptoms | Subtypes | Number of patients | Proportion (n/34) |
|---|---|---|---|
| Infection 29/34 (85.3%) | Respiratory tract infection | 25 | 73.5% |
| Mucocutaneous ulcerated | 4 | 11.8% | |
| Digestive tract infection | 9 | 26.47% | |
| Poliomyelitis | 2 | 5.8% | |
| Fever | 9 | 26.5% | |
| Concomitant autoimmune diseases 13/34 (38.2%) | SLE or SLE? | 8 | 23.5% |
| Hashimoto's thyroiditis | 2 | 5.9% | |
| Hypothyroidism | 1 | 2.9% | |
| Still | 1 | 2.9% | |
| CTD | 1 | 2.9% | |
| Allergy 6/34 (17.6%) | Photoallergy | 1 | 2.9% |
| Drug allergy | 5 | 14.7% | |
| Tumor 3/34 (8.8%) | Retinoblastoma | 1 | 2.9% |
| Pleuropulmonary blastoma | 1 | 2.9% | |
| Lymphoma? | 1 | 2.9% | |
| Involved systems | Nervous system | 7 | 20.6% |
| Vision | 5 | 14.7% | |
| Auditory sense | 1 | 2.9% | |
| Articulation | 9 | 26.5% | |
| Digestive tract | 9 | 26.5% | |
| Renal involvement | 12 | 35.3% | |
| Liver | 7 | 20.6% | |
| hematological system | 7 | 20.6% | |
| Other symptoms | lymphadenectasis | 6 | 17.6% |
| Abdominal mass | 1 | 2.9% |