Figure 22.
Findings for an EAS patient with homozygous CDH23 mutations. A: Pedigree of the patient with CDH23 mutations. B: Preoperative audiogram at age 51. C: Preoperative audiogram at age 53. His hearing showed deterioration at 500 Hz. D: Hearing thresholds four years after cochlear implantation. Residual hearing in lower frequencies was well preserved. E: Postoperative CT imaging and estimated electrode position. F: Speech perception score at age 54 showing good outcome.