Figure 24.

Findings for an EAS patient with MYO7A mutations. A: Pedigree and mutations. B: Hearing thresholds at four years of age. C: Hearing thresholds at nine years of age (pre‐op). Hearing at 1,000 Hz and 2,000 Hz was deteriorated. D: Hearing thresholds six months after cochlear implantation. Residual hearing in lower frequencies was well preserved. E: Hearing thresholds with CI and hearing aid. F: Speech perception test results were dramatically improved after CI.