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. 2020 Feb 6;303(3):563–593. doi: 10.1002/ar.24360

Figure 31.

Figure 31

The EAS patient with TMPRSS3 mutations. A: The patient has compound heterozygous TMPRSS3 mutations, and the parents were found to be carriers for these mutations. B: X‐ray imaging after bilateral EAS. C: Preoperative audiogram. D: Postoperative audiogram (left: 24 months after first EAS, right: four months after second EAS). E: Hearing threshold with bilateral EAS. F: Japanese monosyllable test (65 dB SPL in quiet) showing dramatic improvement with bilateral EAS (A‐F; Miyagawa et al., 2013). G: After bilateral EAS, the sound localization ability with bilateral EAS improved. H: Speech perception in quiet and noise improved (G, H; Moteki et al., 2015).