Table 1.

Main HLA associations with IgG4-mediated neurological diseases

Autoantibody	HLA	Carriers	References
Anti-Musk	DQB1*05	78%	[61]
	DQB1*05-DRB1*14	26%	[61]
	DQB1*05-DRB1*16	20%	[61]
Anti-NF	DRB1*15	77%	[69]
Anti-IgLON5	DQB1*05:01-DRB1*10:01	57–90%	[70, 71, 76]
	DQA1*01-DQB1*05	≈ 90%	[76]
Anti-LGI1	DRB1*07:01	≈ 90%	[84–86]
Anti-CASPR2	DRB1*11:01	48%	[86]

CASPR2 Contactin-associated protein-like 2, HLA Human leukocyte antigen, LGI1 leucine-rich glioma-inactivated 1, MusK muscle-specific tyrosine kinase, NF neurofascin 155