Age (years) |
39.5 (12.7) |
Gender (male/female) |
3/16 |
Race (white/other) |
18/1 |
Weight (kg) |
65.2 (14.7) |
Height (cm) |
160.7 (8.0) |
Body mass index (BMI, kg/m2) |
25.3 (5.7) |
PAH etiology (%) |
|
Idiopathic |
4 (21.1%) |
Collagen vascular disease |
2 (10.5%) |
HIV |
5 (26.3%) |
Congenital heart disease with shunt |
7 (36.8%) |
Portopulmonary hypertension |
1 (5.3%) |
World Health Organization functional class (%) |
|
Class 1 |
9 (47.4%) |
Class 2 |
5 (26.3%) |
Class 3 |
3 (15.8%) |
Class 4 |
2 (10.5%) |
6-minute walk distance (m) |
437 (89) |
Echocardiographic data |
|
Transtricuspid gradient (mmHg) |
71 (27) |
Systolic pulmonary arterial pressure (mmHg) |
76.4 (28.1) |
Tricuspid annular plane systolic excursion (cm) |
17.5 (3.0) |
Right ventricular diameter (M module, cm) |
3.4 (1.0) |
Right heart catheterization |
|
Mean pulmonary arterial pressure (mmHg) |
57.4 (16.7) |
Pulmonary artery occlusion pressure (mmHg) |
8.8 (4.3) |
Cardiac output (L/minute) |
5.1 (2.0) |
Pulmonary vascular resistance (Woods unit) |
11.5 (8.7) |
Right Arterial Pressure (mmHg) |
8.8 (5.3) |
Pulmonary arterial hypertension therapy |
|
None |
2 (10.5%) |
Phosphodiesterese type 5 inhibitors |
16 (84.2%) |
Endothelin antagonists |
7 (36.8%) |
Prostanoids |
1 (5.3%) |