AAT	Alpha 1-antitrypsin
AATD	Alpha 1-antitrypsin deficiency
PN	Proteostasis network
ER	Endoplasmic reticulum
ERAD	ER-associated degradation
NSPs	Neutrophil serine proteases
RCL	Reactive center loop
PAS + D	Periodic acid–Schiff-positive diastase
GS1 and GS2	Glucosidase I and II
CNX	Calnexin
ERGIC53	Endoplasmic reticulum–Golgi intermediate compartment
ERp57	Calnexin–endoplasmic reticulum protein 57
GRP94	Glucose-regulated protein 94
UGGT1	Uridine diphosphate (UDP)-glucose:glycoprotein glucosyltransferase 1
ERManI	ER α-mannosidase I
EDEM	ER degradation-enhancing α-mannosidase-like proteins
HRD1	HMG-CoA reductase degradation 1 homolog
HERPUD1	Homocysteine inducible ER protein with ubiquitin-like domain 1
UPS	Ubiquitin–proteasome system
DUBs enzyme	Deubiquitinilating enzyme
CBZ	Carbamazepine
TFEB	Transcription factor EB master gene
ERLAD	ER-to-lysosome-associated degradation
UPR	Unfolded protein response
CF	Cystic fibrosis
CFTR	Cystic fibrosis transmembrane conductance regulator
4-PBA	Sodium 4-phenylbutyrate
SAHA	Suberoylanilide hydroxamic acid