Ang-1	Angiopoietin 1
APAH	associated PAH
BPA	Balloon pulmonary angioplasty
BMPR2	Bone morphogenetic protein receptor type II
BMPs	Bone morphogenetic proteins
tacrolimus	Calcineurin inhibitor FK506
CCL	Chemokine C-C motif ligand
CXCL	Chemokine C-X3-C motif ligand
CTEPH	Chronic thromboembolic pulmonary hypertension
CHD	Congenital heart disease
CTD-PAH	Connective tissue disease associated PAH
DC-SIGN	Dendritic cell- specific intercellular adhesion molecule-3 grabbing non- integrin
DCs	Dendritic cells
DMF	Dimethyl fumarate
Tfh	Follicular T-helper cells
FC	Functional class
γδ	Gamma delta
HPAH	Heritable PAH
TCRs	Heterodimeric T-cell receptors
HIF-1α	Hypoxia-inducible factor-1α
IPAH	Idiopathic PAH
IL	Interleukin
LTB4	Leukotriene B4
CCL3	Macrophage inflammatory protein-1α
MHC	Major histocompatibility complex
MCs	Mast cells
MMP-9	Matrix metallopeptidase 9
MCTD	Mixed connective tissue diseases
MCT	Monocrotaline
mo-DCs	Monocyte-derived DCs
MPO	Myeloperoxidase
NIAD	National Institute of Allergy and Infectious Diseases
NK	Natural killer cells
NYHA	New York Heart Association
NF-κβ	Nuclear factor kappa-light-chain-enhancer of activated B cells
NFAT	Nuclear factor of activated T cell
Porto-pulmonary PAH	PAH due to liver disease
PPHN	Persistent pulmonary hypertension of the newborn
PlGF	Placental growth factor
pDCs	Plasmacytoid DCs
PAH	Pulmonary arterial hypertension
PAP	Pulmonary arterial pressures
PASMCs	Pulmonary arterial smooth muscle cells
PEA	Pulmonary endarterectomy
PH	Pulmonary hypertension
PVR	Pulmonary vascular resistance
PVOD	Pulmonary veno-occlusive disease
ROS	Reactive oxygen species
RELMα	Resistin-like molecule-α
RV	Right ventricular
RVH	Right ventricular hypertrophy
SU/Hx	Sugen/hypoxia
SLE	Systemic lupus erythematosus
SSc	Systemic sclerosis
TLOs	Tertiary lymphoid organs
Th	T-helper cell
TSP-1	Thrombospondin-1
TNFAIP3	TNF Alpha Induced Protein 3
NRF2	Transcriptional regulator nuclear factor erythroid 2-related factor 2
TGF-β	Transforming growth factor beta
TNF-α	Tumor necrosis factor alpha
cDC1s	Type 1 conventional DCs
cDC2s	Type 2 cDCs
VEGF	Vascular endothelial growth factor