Skip to main content
. 2019 Feb 26;39(Suppl 1):1–151. doi: 10.1007/s10875-019-00597-5
Demographics Number of patients % USIDNET CVID cohort 95%Confidence Interval
Gender:
Male 638 41.3% 0.39-0.43
Female 908 58.7% 0.56-0.60
Age group:
<10 years 16 1% Median age 50 years
10-20 years 188 12% Mean 47.6 years
20-35 years 300 19% CI 46.6-48.74 for mean
35-55 years 415 27%
>=55 years 627 41%
Race:
Caucasian 1283 96% 0.95-0.97
Others (African-American, Asian, Hispanic) 34 3% 0.01-0.03
Unknown 1% 0.05-0.01
Living 1415 91.5% 0.95-0.97
Deceased 55 3.5% 0.03-0.02
Lost follow up 76 5%
Family history of PIDD
Yes 176 11.38% 0.20-0.26
No 575 37.2% 0.73-0.79
Unknown 795 51.4%