Table 4.
Group A: patients treated with local therapy or systemic therapy ‘less than CHOP’
Pat. | Age/sex | Cutaneous manifestations | Extracutaneous manifestations | Initial therapy | CR/PR | Survival (months) |
---|---|---|---|---|---|---|
2 | 63/m | + | + | COP | No | 61/2 |
3 | 47/f | + | − | RT, PUVA, IFN-α | No | 17+ (AWD) |
4 | 81/f | + | + | Prednisone | PR | 10 |
5 | 82/m | + | + | COP+mitoxantrone | CR | 8 |
6 | 79/m | + | + | Prednisone | CR | 3 |
8 | 72/m | + | + | RT | No | 5 |
12 | 89/m | + | − | IL-2, RT | CR | 20 |
15 | 21/f | + | − | RT | CR | 18+ |
16 | 86/f | + | + | COP | CR | 5 |
18 | 67/f | + | − | COP-C | CR | 17 |
19 | 84/m | + | + | CP | CR | 5 |
20 | 65/f | + | + | COP-C | CR | 17 |
25 | 83/m | + | + | COP | No | 19 |
26 | 89/f | + | + | RT | PR | 5 |
27 | 82/m | + | + | Etoposide + prednisone +IFNα/γ | CR | 8 |
36 | 67/f | + | − | COP-C | CR | 16 |
49 | 76/m | − | + | Symptomatic | No | 3 |
51 | 81/f | + | + | COP | CR | 12 |
53 | 69/m | + | + | COP | CR | 12 |
58 | 79/m | + | − | Cyclophosphamide, etoposide, Prednisone | CR | 8 |
67 | 67/m | + | + | 6-Mercaptopurine, MTX, prednisone | PR | 12+ |
68 | 70/m | + | + | COP | CR | 7 |
70 | 79/m | + | + | Vincristine, prednisone | CR | 6 |
77 | 86/m | + | − | RT | CR | ND |
87 | 64/m | + | + | CEP | CR | 6+ (PD) |
88 | 88/f | + | − | HU | No | 8 |
89 | 72/m | + | + | Cyclophosphamide, MTX, vincristine + i.th. | CR | 14+ |
90 | 81/m | + | − | RT | CR | 22+ (AWD) |
n=28 | Med. 79 | 27/28 96% | 19/28 68% | 19CR 68% | Med. OS 9 | |
m:f 18:10 | 3PR 11% | CR at last follow-up 2/28 (7%) |
AWD: alive with disease; CEP: cyclophosphamide, eldisine, prednisolone; COP: cyclophosphamide, vincristine, prednisone; COP-C: COP+ chlorambucil; HU: hydroxyurea; IFN-α: interferon-alpha; IFN-γ: interferon-gamma; IL-2: interleukin-2; i.th: intrathecal; MTX: methotrexate; PUVA: psoralen plus ultraviolet A therapy; RT: radiotherapy; CR: complete remission; PR: partial remission; ND: not determined.