Skip to main content
. 2013 May 15;36(4):645–658. doi: 10.1007/s10545-013-9611-5

Fig. 3.

Fig. 3

Fibroblast fatty acid oxidation flux using palmitate in 9 myopathic CPT2 deficient cell lines and 3 neonatal CPT2 deficient cell lines grown and assayed at 37oC and 41oC. The lower fatty acid oxidation flux in all the myopathic cell lines demonstrates the thermal instability of the CPT2 mutant protein at higher temperature. Neonatal “severe” CPT2 deficient cell lines show barely detectable flux at both temperatures. (Olpin et al 2003)