Fig. 4.

Mitochondrial FAD dependent pathways. FAD co-factor dependent acyl-CoA dehydrogenases, ETF, ETFDH and other FAD containing proteins including complexes I and II of the respiratory chain. Relationship of fatty acid oxidation, amino acid degradation and the respiratory chain. FMN flavin mononucleotide. FAD flavin adenine dinucleotide. ETF electron transfer flavoprotein. SCAD short chain acyl-CoA dehydrogenase. MCAD medium chain acyl-CoA dehydrogenase. LCAD long chain acyl-CoA dehydrogenase. VLCAD very long chain acyl-CoA dehydrogenase. ACAD9 acyl-CoA dehydrogenase 9. ACAD10/11 acyl-CoA dehydrogenase 10/11. GCD glutaryl-CoA dehydrogenase. D-2-HGD D-2-hydroxyglutaryl-CoA dehydrogenase. IVD isovaleryl-CoA dehydrogenase. SBCAD short branched chain acyl-CoA dehydrogenase. IBD isobutyryl-CoA dehydrogenase. DMGD dimethylglycine dehydrogenase. SARD sarcosine dehydrogenase