Table 4.
Types | Behavior | Frequency (%) | Percent (%) 5-year survival |
---|---|---|---|
Mycosis fungoides (MF) | Indolent | 44 | 88 |
Folliculotropic MF | Indolent | 4 | 80 |
Pagetoid reticulosis | Indolent | <1 | 100 |
Granulomatous slack skin | Indolent | <1 | 100 |
Sezary syndrome | Aggressive | 3 | 24 |
Adult T-cell leukemia and lymphoma | NA | NA | NA |
Primary cutaneous CD30+ lymphoproliferative disorders | |||
Primary cutaneous ALCL | Indolent | 8 | 95 |
Lymphomatoid papulosis | Indolent | 12 | 100 |
Subcutaneous panniculitis-like T-cell lymphoma | Indolent | 1 | 75 |
Extranodal NK/T-cell lymphoma, nasal type | Aggressive | <1 | NR |
Primary cutaneous peripheral T-cell lymphoma, nos | Aggressive | 2 | 16 |
Primary cutaneous aggressive epidermotropic CD8+ T-cell lymphoma | Aggressive | <1 | 18 |
Primary cutaneous CD4+ small/medium pleomorphic T-cell lymphoma | Indolent | 2 | 75 |