Table 2.
Classification of primary vasculitides according to the Chapel Hill Consensus Conference [2]
| I. Large vessel vasculitis |
| 1. Giant cell (temporal) arteritis |
| 2. Takayasu arteritis |
| II. Medium-sized vessel vasculitis |
| 1. Polyarteritis nodosa |
| 2. Kawasaki disease |
| III. Small vessel vasculitis |
| 1. Wegener’s Granulomatosis⁎ |
| 2. Churg–Strauss syndrome⁎ |
| 3. Microscopic polyangiitis⁎ |
| 4. Henoch Schönlein purpura |
| 5. Essential cryoglobulinemia vasculitis |
| 6. Cutaneous leukocytoclastic angiitis |
ANCA-associated.