Table 2.

Clinical-demographic characteristics at baseline in the whole cohort and in the hereditary/sporadic subgroups

	Whole cohort (n = 42)	Hereditary (n = 23)	Sporadic (n = 19)	Statistic
Age at examination	53 ± 13	47 ± 12	61 ± 10	0.67
Sex (females, %)	13 (31%)	6 (25%)	7 (39%)	0.52
Age at onset	46 (28;56)	33 ± 15	53 ± 8	0.003
Disease duration	10 (3;15)	13 (7;19)	3 (2;14)	0.008
Death during follow-up (no. of cases)	2 (4.7%)	0	2 (10.5%)	0.2
SARA	13.5 (9;17.5)	14 ± 7	14 ± 5	0.08
UMSARS I	7.5 (5;12)	5 (3;10)	9 (6;14)	0.04
UMSARS II	16.3 ± 7.4	12 (10;19)	19 (12;21)	0.29
SCOPA-Aut	7 (3;14)	4 (3;12)	12 (7;15)	0.03
OHQ	0 (0;4)	0 (0;2.5)	0 (0;5.3)	0.32

Statistically significant differences are reported in bold