Table 1.
Characteristics | Median [IQR] or N (%) | |||||
---|---|---|---|---|---|---|
JDM (n = 57) | CANDLE (n = 11) | SAVI (n = 7) | NOMID (n = 18) | HC (n = 26) | ||
Age at evaluation (year) | 9.5 [5.9–13.2] | 6.1 [5.2–15.7] | 16.9 [6.1–18.1] | 8.5 [5.3–17.1] | 25.9 [9.7–39.4] | |
Gender | Female | 34 (60) | 5 (45) | 3 (43) | 7 (39) | 17 (65) |
Race | White | 36 (63) | 4 (36) | 7 (100) | 12 (67) | 15 (58) |
Hispanic | 4 (7) | 4 (36) | 0 | 3 (17) | 8 (31) | |
Black | 3 (5) | 2 (18) | 0 | 1 (6) | 1 (4) | |
Multiple race | 10 (18) | 0 | 0 | 1 (6) | 1 (4) | |
Other | 4 (7) | 1 (9) | 0 | 1 (6) | 1 (4) | |
Disease duration (months) | 10.7 [4.9–36.7] | NA | NA | NA | NA |
Abbreviations: IQR interquartile range, NA not applicable, JDM juvenile dermatomyositis, CANDLE Chronic Atypical Neutrophilic Dermatosis with Elevated temperature, SAVI STING-Associated Vasculopathy with onset during Infancy, NOMID Neonatal-onset multisystem inflammatory disease, HC healthy controls