Table 1.

Demography, Clinical and Laboratory Characteristics of COHARD-PH Registry Patients

Characteristics	Total (n = 1012)
Age at First Enrollment (years) [mean ± SD]	34.7 ± 13.2
Body Mass Index [mean ± SD]	19.9 ± 7.7
Underweight [n(%)]	417 (41.2)
Blood Pressure (mmHg) [mean ± SD]
Systolic	111.9 ± 16.4
Diastolic	72.9 ± 11.4
Oxygen Saturation (%)[mean ± SD]a	95.5 ± 5.3
6 Minute Walk Distance (meter)[mean ± SD]b	356.5 ± 99.9
WHO Functional Class [n(%)]c
I	418 (41.9)
II	435 (43.0)
III	101 (10.0)
IV	11 (1.1)
Hemoglobin (g/dL) [mean ± SD]d	13.8 ± 2.2
Hematocrit (%) [mean ± SD]e	42.1 ± 16.2
NTproBNP (pg/mL) [median (IQR)]f	370.9 (132.3–1625.0)
Pulmonary hypertension (by TTE) [n(%)]	780 (77.1)
Eisenmenger Syndrome [n (%)]	189 (18.7)
Post Defect Closure [n (%)]	24 (2.9)

^a data of 736 patients; ^b data of 616 patients; ^c data of 965 patients; ^d data of 574 patients; ^e data of 586; ^f data of 405 patients