Table 1.

Differential diagnosis of arrhythmogenic right ventricular cardiomyopathy

Mimics of right-dominant ARVC

Primary arrhythmia conditions

Right ventricular outflow tract tachycardia

Brugada syndrome

Structural diseases

Congenital heart diseases (left to right shunt, Ebstein’s anomaly, Uhl’s anomaly)

Pulmonary artery hypertension

Athlete’s heart

Chest deformity and pericardial absence

Mimics of left-dominant ARVC

Structural diseases

Dilated cardiomyopathy

Neuromuscular cardiomyopathies (muscular dystrophies and myofibrillar myopathies)

Myocarditis

Cardiac sarcoidosis

Congenital ventricular aneurysms

Chagas’ heart disease