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. 2020 Mar 24;21(6):2256. doi: 10.3390/ijms21062256
GAA acid α-glucosidase
IPD Infantile Onset Pompe Disease
LOPD Late Onset Pompe Disease
ERT Enzyme Replacement Therapy
rhGAA recombinant human GAA
hGAA human GAA
XII Hypoglossal
WBPPAS+ Whole Body PlethysmographyPositive Periodic Acid-Schiff
CtB Cholera Toxin B
ChAT Choline Acetyltransferase
IBA-1 Ionized Calcium Binding Adaptor Molecule 1
GFAP Glial Fibrillary Acidic Protein
TUNEL Terminal Deoxynucleotidyl Transferase dUTP Nick and Labeling
WT Wild Type
CC3 Cleaved Caspase 3
NTS Nucleus of the Solitary Tract
Te Expiratory Time
TV Tidal Volume
Te Expiratory Time
f Frequency
TV/Ti Ratio of Tidal Volume to Inspiratory Time
VE Minute Ventilation
VE/VCO2 Ratio of Minute Ventilation to Expired CO2
PIF Peak Inspiratory Flow
PEF Peak Expiratory Flow
PaO2 Partial Pressure of Oxygen