GAA |
acid α-glucosidase |
IPD |
Infantile Onset Pompe Disease |
LOPD |
Late Onset Pompe Disease |
ERT |
Enzyme Replacement Therapy |
rhGAA |
recombinant human GAA |
hGAA |
human GAA |
XII |
Hypoglossal |
WBPPAS+ |
Whole Body PlethysmographyPositive Periodic Acid-Schiff |
CtB |
Cholera Toxin B |
ChAT |
Choline Acetyltransferase |
IBA-1 |
Ionized Calcium Binding Adaptor Molecule 1 |
GFAP |
Glial Fibrillary Acidic Protein |
TUNEL |
Terminal Deoxynucleotidyl Transferase dUTP Nick and Labeling |
WT |
Wild Type |
CC3 |
Cleaved Caspase 3 |
NTS |
Nucleus of the Solitary Tract |
Te |
Expiratory Time |
TV |
Tidal Volume |
Te |
Expiratory Time |
f |
Frequency |
TV/Ti |
Ratio of Tidal Volume to Inspiratory Time |
VE |
Minute Ventilation |
VE/VCO2
|
Ratio of Minute Ventilation to Expired CO2
|
PIF |
Peak Inspiratory Flow |
PEF |
Peak Expiratory Flow |
PaO2
|
Partial Pressure of Oxygen |