Table 33–1.

Criteria for the diagnosis of Kawasaki disease

Fever for more than five days (four days if treatment with intravenous immunoglobulin eradicates fever) plus at least four of the following clinical signs not explained by another disease process: •Bilateral conjunctival injection (80% to 90%)∗ •Changes in the oropharyngeal mucous membranes, including one or more of injected and/or fissured lips, strawberry tongue, injected pharynx (80% to 90%) •Changes in the peripheral extremities, including erythema and/or edema of the hands and feet (acute phase) or periungual desquamation (convalescent phase) (80%) •Polymorphous rash, primarily truncal; nonvesicular (>90%) •Cervical lymphadenopathy with at least one node >1.5 cm (50%)

^∗Numbers in parentheses indicate the approximate percentage of children with Kawasaki disease who demonstrate the criterion.

^∗ Modified from Centers for Disease Control: Revised diagnostic criteria for Kawasaki disease, MMWR Morb Mortal Wkly Rep 39:27-28, 1990.