Figure 3.
AE diagnostic process.
Abbreviations: AE, angioedema; BK-AE, bradykinin mediated angioedema; MC-AE, mast cell angioedema; nC1INH-HAE, hereditary angioedema with normal C1-inhibitor; ACEi, angiotensin-converting enzyme inhibitors; INMC-AE, idiopathic non-mast cell angioedema; NSAID, nonsteroid anti-inflammatory drugs; FXII, Hageman factor gene; PLG, plasminogen gene; C1Inh, C1Inhibitor.