Table 3.

Magnetic resonance imaging findings.

	Total		Subgroup by age at onset				P-value
			Age ≤ 2yr (n = 89)		Age > 2yr (n = 21)
Basal ganglia	104	94.5 (%)	84	94.4 (%)	20	95.2 (%)	0.678
Thalamus	38	34.5 (%)	33	37.1 (%)	5	23.8 (%)	0.071
Brainstem	45	40.9 (%)
Midbrain	44	40.0 (%)	35	39.3 (%)	9	42.9 (%)	0.766
Pons	27	24.5 (%)	22	24.7 (%)	5	23.8 (%)	0.931
Medulla	30	27.3 (%)	23	25.8 (%)	7	33.3 (%)	0.488
Number of brain stem parts involved							0.067
0	62	56.4 (%)	51	57.3 (%)	11	52.4 (%)
1	17	15.5 (%)	15	16.9 (%)	2	9.5 (%)
2	10	9.1 (%)	5	5.6 (%)	5	23.8 (%)
3	21	19.1 (%)	18	20.2 (%)	3	14.3 (%)
Cerebellum	41	37.3 (%)	35	39.3 (%)	6	28.6 (%)	0.359
Cerebral atrophy	64	58.2 (%)					0.332
Mild	49	44.5 (%)	40	44.9 (%)	9	42.9 (%)
Severe	15	13.6(%)	14	15.7 (%)	1	4.8 (%)
Cortex signal abnormality	33	30.0 (%)	28	31.5 (%)	5	23.8 (%)	0.491
White matter signal abnormality	42	38.2 (%)					0.524
Mild	40	36.4 (%)	34	38.2 (%)	6	28.6 (%)
Severe	2	1.82 (%)	2	2.2 (%)	0	0.0 (%)