Table 2.
Difference analysis in clinical features between children and adults in 63 Chinese case reports.
| Clinical features | Children (N = 30) n (%) |
Adults (N = 33) n (%) |
p value |
|---|---|---|---|
| Abnormal liver function | 5 (17%) | 9 (27%) | 0.312 |
| Liver transplant | 4 (13%) | 4 (12%) | 1.00 |
| Partial hepatectomy | 5 (17%) | 6 (18%) | 0.874 |
| Hepatomegaly | 17 (57%) | 7 (21%) | 0.004 |
| Splenomegaly | 21 (70%) | 22 (67%) | 0.777 |
| Splenectomy | 3 (10%) | 8 (24%) | 0.137 |
| EGVB | 15 (50%) | 19 (58%) | 0.547 |
| Ascites | 5 (17%) | 10 (30%) | 0.204 |
| Polycystic kidneys | 8 (27%) | 16 (48%) | 0.075 |
| Medullary sponge kidneys | 4 (13%) | 3 (9%) | 0.700 |
| Bile duct abnormalities | 13 (43%) | 19 (58%) | 0.259 |
| Portal vein malformations | 3 (10%) | 3 (9%) | 1.000 |
| Other systems | 4 (13%)† | 7 (21%)†† | 0.411 |
EGVB = esophageal and gastric variceal bleeding. †Four cases including pulmonary interstitial fibrosis, uterine and kidney malformation, patent ductus arteriosus, and arachnoid cyst. ††Seven cases including arachnoid cyst and cerebral dysplasia, cerebral aneurysm, polycystic ovary syndrome, breast dysplasia, duodenal diverticulum tumor, macular degeneration, and IgG4-related autoimmune pancreatitis.