Table 1. The clinical characteristics of patients with IgG4-related sclerosing cholangitis.

Parameter (n = 69)
Age, mean ± SD, years	66.1 ± 10.5
Sex, male / female (%)	60 (87.0) / 9 (13.0)
Accuracy of diagnosis, definite / probable	68 (98.6) / 1 (1.4)
Obstructive jaundice†, present / absent (%)	32 (46.4) / 37 (53.6)
Serum IgG level, median (range), mg/dl	1871.5 (950–5963)
Serum IgG4 level, median (range), mg/dl	484 (145–4080)
Cholangiography findings, type 1 / 2 / 3 / 4	55 / 5 / 7 / 2
Concurrence of autoimmune pancreatitis, diffuse / focal / absent	48 / 20 / 1
Endoscopic biliary drainage, present / absent (%)	28 (40.6) / 41 (59.4)
CS maintenance therapy‡, present / absent (%)	64 (92.8) / 5 (7.2)
Maintenance dose of prednisolone, median (range), mg/day	5 (1–10)
Follow-up period§, median (range), months	65.3 (7.0–192.1)

† Serum total bilirubin level of > 3.0 mg/dL with dilation of bile-duct.

‡ Maintenance therapy was defined as continuous administration of CS for > 6 months after initiation.

§ Follow-up period counts from CS initiation.

CS, corticosteroid therapy.