Table 1.

Biochemical testing

Patient	C4 g/L (0.1–0.4)	C1-INH protein g/L (0.21–0.39)	C1-INH function (0.70–1.30)
Index patient	0.06	0.10	0.16
Father	0.20	0.06	0.41
Sister	0.13	0.08	0.5

C1-INH, C1-inhibitor.