TABLE 2.
Characteristics of the population.
| ALS | ALS/FTD | FTD | Sporadic ALS | |
| n | 118 | 37 | 32 | 999 |
| Gender: M/F (ratio) | 56/62 (0.9)a | 22/15 (1.46)a | 14/18 (0.78) | 555/444 (1.25) |
| Bulbar onset (%) | 39 | 36.1 | – | 35.7 |
| UL onset (%) | 18 | 16.6 | – | 25.0 |
| LL onset (%) | 43 | 41.7 | – | 39.3 |
| Dementia onset (%) | – | 5.6 | – | – |
| Age at onset | 57.5 ± 10.4b | 60.4 ± 7.0c | 65.7 ± 9.4 | 65.7 ± 11.8 |
| n | 94 | 34 | 10 | 999 |
| Age at death | 60.7 ± 10.0 | 63.7 ± 6.7 | 72.3 ± 8.5 | 68.8 ± 11.5 |
| n | 86 | 30 | 13 | 999 |
| Disease duration | 40.3 ± 24.4a | 30.0 ± 18.2a | 87.6 ± 35.7 | 37.2 ± 31.7 |
| Median survival | 33.5 | 26.4 | 75 | 29.6 |
| n | 86 | 29 | 8 | 999 |
M/F, male/female; UL, upper limb; LL, lower limb. aNot statistically different vs. sporadic ALS cases. bvs. sporadic ALS: p < 0.0001. cvs. sporadic ALS: p = 0.008.