TABLE 3.

Clinical characteristics of ALS and ALS/FTD patients.

	Age of onset	Age at death	Disease duration	ALSFRS-R score
ALS
Bulbar onset	59.4 ± 10.0(33)	61.1 ± 10.8(30)	37.0 ± 28.7(30)	39.0 ± 3.6(25)
UL onset	56.4 ± 10.7(16)	58.5 ± 9.1(14)	42.1 ± 30.6(14)	35.6 ± 9.5(9)
LL onset	56.3 ± 10.5(35)	59.9 ± 10.7(32)	43.3 ± 19.8(32)	40.0 ± 4.5(24)
ALS/FTD
Bulbar onset	60.0 ± 9.4(12)	63.8 ± 8.8(10)	22.6 ± 9.1(10)	38.5 ± 8.1(11)
UL onset	59.3 ± 5.8(6)	61.4 ± 5.3(5)	39.4 ± 26.4(5)	31.4 ± 16.8(6)
LL onset	61.0 ± 5.9(14)	64.7 ± 6.0(12)	30.7 ± 18.1(12)	36.6 ± 11.0(9)
Dementia onset	61.0 ± 4.8(2)	64.3 ± 7.3(2)	39.8 ± 30.5(2)
ALS
Men	56.7 ± 10.6(45)	60.0 ± 10.1(38)	35.8 ± 19.0(37)	39.6 ± 5.3(32)
Women	58.0 ± 10.2(48)	60.9 ± 10.1(46)	43.7 ± 27.7(49)	37.9 ± 5.9(26)
ALS/FTD
Men	59.4 ± 6.6(21)	62.5 ± 6.5(18)	30.5 ± 17.6(18)	40.0 ± 6.7(15)
Women	61.9 ± 7.6(13)	65.5 ± 6.9(12)	29.2 ± 19.9(11)	31.8 ± 14.0(11)

Values are means ± SD (n). ALSFRS-R, amyotrophic lateral sclerosis rating scale-revised; UL, upper limb; LL, lower limb.