Table 1.
Demographics of Patients with ALS
| Patient | Age (years) | Sex | ALS Mutation | Months from Diagnosis | Muscle (Biopsies Were Done on Limb Muscle where the Disease Began) | Patient Information |
|---|---|---|---|---|---|---|
| 1 | 47 | F | SOD1D90A | 12 | soleus dx | Spinal onset |
| 2 | 72 | F | Sporadic | 42 | vastus lateralis dx | Spinal onset |
| 3 | 50 | M | VCP mutation | 54 | vastus lateralis dx | Spinal onset with IBM (inclusion body myositis) and Paget's disease |
| 4 | 62 | F | C9ORF72 (58 repeats) | 33 | soleus dx | Spinal onset with progressive muscle atrophy |
| 5 | 77 | F | Sporadic | 19 | vastus lateralis dx | Spinal onset |
| 6 | 71 | F | Sporadic | 14 | rectus femoris dx | N/A |