Table 1.
Clinical characteristics of study patients.
| N. | % | |
|---|---|---|
| Index patients | 212 | |
| Italians | 190 | 89.6 |
| Women | 113 | 53.3 |
| Positive family history (n = 193) | 148 | 76.7 |
| Presence of liver cysts (n = 159) | 128 | 80.5 |
| Vascular abnormalities (n = 121) | 24 | 19.8 |
| Urological events before 35 yr (n = 128) | 34 | 26.6 |
| Antihypertensive treatment before 35 yr (n = 133) | 54 | 40.6 |
| ESRD (n = 165) | 42 | 25.5 |
| Transplantation (n = 177) | 45 | 25.4 |
| ADPKDVEO (n = 163) | 7 | 4.3 |
| ADPKDEO (n = 163) | 23 | 14.1 |
| Median value | ||
| Age at test, yr (n = 212) | 50 | |
| Age at onset, yr (n = 163) | 25 | |
| Age at diagnosis, yr (n = 156) | 41 | |
| Serum creatinine at presentation, mg/dl (n = 155) | 1.15 | |
| GFR at presentation, ml/min (n = 131) | 66 |
The number of cases for which the data was available is shown in brackets. ESRD, End-Stage Renal Disease; GFR, Glomerular Filtration Rate; VEO, Very Early Onset (diagnosed in utero or before 18 months); EO, Early Onset (diagnosed before 15 years).