Table 2:
Diagnostic Test | Full Cohort | Delinite CS | Probable CS | Possible CS |
---|---|---|---|---|
(n = 77) | (n = 11) | (n =31) | (n = 35) | |
Extracardiac pathology | ||||
Extracardiac biopsy | 34 (44) | 2 | 31 | 1 |
Positive cxtracardiac biopsy | 33 (97) | 2 | 31 | 0 |
Cardiac pathology | ||||
Cardiac biopsy | 19 (25) | 6 | 6 | 7 |
Positive cardiac biopsy | 5 (26) | 5 | 0 | 0 |
LVAD-related tissue | 3 (4) | 2 | 0 | 1 |
Positive LVAD-rclated tissue | 2 (67) | 2 | 0 | 0 |
Heart transplant | 11 (14) | 7 | 2 | 2 |
Positive explanted cardiac tissue | 7 (64) | 7 | 0 | 0 |
Diagnosis made after transplant | 6 (8) | 6 | 0 | 0 |
Cardiac imaging | 72 (94) | 6 | 31 | 35 |
FDG-PET only | 35 | 3 | 16 | 16 |
CMR only | 1 | 1 | 0 | 0 |
FDG-PET and CMR | 36 | 2 | 15 | 19 |
FDG-PET negative. CMR positive | 0 | 0 | 0 | 0 |
CMR negative, FDG-PET positive | 5 | 0 | 1 | 4 |
Echocardiography | 77 (100) | 11 | 31 | 35 |
Initial LVEF at time of diagnosis (mean), % | 43 | 38 | 48 | 43 |
Worse LVEF at any time (mean), % | 35 | 22 | 38 | 37 |
Most current LVEF (mean), % | 48 | 58 | 49 | 46 |
Angiotensin converting enzyme checked (ever) | 42 (55) | 5 | 22 | 15 |
Elevated ACE (ever) | 10 (24) | 1 | 6 | 3 |
Immunoglobulin levels checked (ever) | 19 (25) | 3 | 7 | 9 |
Elevated immunoglobulins (ever) | 2 (11) | 0 | 0 | 2 |
Data are number (%) except for LVEF, angiotensin converting enzyme, and immunoglobulins, which are mean (SD). CS = cardiac sarcoidosis; LVEF = left ventricular ejection fraction.