Figure 4.

Audiological assessment in an adult patient with auditory neuropathy spectrum disorder (ANSD) and bilateral cochlear nerve atrophy. Unaided thresholds for pure-tone audiometry ((a), black line for right ear, gray line for left ear) and speech audiometry ((b), black line for right ear, gray line for left ear) in quiet are good. Otoacoustic emissions (OAEs) are present bilaterally in both temporal/intensity recordings (left panel in (c) for right ear, left panel in (d) for left ear) and spectral analysis (right panel in (c) for right ear, right panel in (d) for left ear); on the other hand, auditory brainstem responses (ABRs) are abnormal with no clear cochlear microphonic (CM) ((e) for right ear, (f) for left ear).