Figure 9.

Audiological assessment in a 14-years-old male with auditory neuropathy spectrum disorder (ANSD). His medical history includes neonatal hyperbilirubinemia and low birth weight. Despite early hearing aids fitting, speech development was delayed. He shows residual pure-tone hearing thresholds ((a), gray line) and poor speech discrimination ((b), gray line) in the left ear. After left-ear cochlear implantation, aided tonal ((a), black line) and speech ((b), black line) thresholds show good auditory outcomes. Auditory brainstem responses (ABRs) at left ear are absent (c). However, speech perception in noise, such as during school activities, remains poor.