Table 1.
Clinical Variables of Fresh Frozen MPNST Collected by GeM Consortium.
| NF1-Related | Sporadic or Unknown Diagnosis | Total MPNST | |
|---|---|---|---|
| n (%) | n (%) | n (%) | |
| Fresh Frozen MPNST | 60 (62.5%) | 36 (39.6%) | 96 (100%) |
| Tumor Grade | |||
| Low Grade | 5 (5.2%) | 2 (2.1%) | 7 (7.3%) |
| High Grade | 49 (51.0%) | 32 (33.3%) | 81 (84.4%) |
| Unknown | 6 (6.3%) | 2 (2.1%) | 8 (8.3%) |
| Neo-Adjuvant Treatment | |||
| Chemotherapy | 8 (8.3%) | 5 (5.2%) | 13 (13.5%) |
| Radiation | 3 (3.1%) | 9 (9.4%) | 12 (12.5%) |
| Chemotherapy and Radiation | 2 (2.1%) | 2 (2.1%) | 4 (4.2%) |
| No neo-adjuvant treatment | 44 (45.8%) | 20 (20.8%) | 64 (66.7%) |
| Unknown | 3 (3.1%) | 0 (0%) | 3 (3.1%) |
| Tumor Anatomic Location | |||
| Head/Neck/Face | 4 (4.2%) | 0 (0%) | 4 (4.2%) |
| Lower Limb | 18 (18.8%) | 18 (18.8%) | 36 (37.5%) |
| Upper Limb | 14 (14.6%) | 12 (12.5%) | 26 (27.1%) |
| Brachial Plexus | 3 (3.1%) | 1 (1.0%) | 4 (4.2%) |
| Lumbosacral Plexus | 5 (5.2%) | 3 (3.1%) | 8 (8.3%) |
| Trunk | 8 (8.3%) | 1 (1.0%) | 9 (9.4%) |
| Retroperitoneum | 1 (1.0%) | 0 (0%) | 1 (1.0%) |
| Other | 7 (7.3%) | 1 (1.0%) | 8 (8.3%) |
| Total MPNST | 60 (62.5%) | 36 (37.5%) | 96 (100%) |